ENTRY       EC 6.4.1.4
NAME        Methylcrotonoyl-CoA carboxylase
CLASS       Ligases
            Forming carbon-carbon bonds
SYSNAME     3-Methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming)
REACTION    ATP + 3-Methylcrotonoyl-CoA + HCO3- = ADP + Orthophosphate +
            3-Methylglutaconyl-CoA
SUBSTRATE   ATP
            3-Methylcrotonoyl-CoA
            HCO3-
PRODUCT     ADP
            Orthophosphate
            3-Methylglutaconyl-CoA
COFACTOR    Biotin
COMMENT     A biotinyl-protein.
PATHWAY     PATH: MAP00280  Valine, leucine and isoleucine degradation
GENES       HSA: MCCC1 MCCC2
DBLINKS     University of Geneva ENZYME DATA BANK: 6.4.1.4
            WIT (What Is There) Metabolic Reconstruction: 6.4.1.4
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