ENTRY EC 6.4.1.4
NAME Methylcrotonoyl-CoA carboxylase
CLASS Ligases
Forming carbon-carbon bonds
SYSNAME 3-Methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming)
REACTION ATP + 3-Methylcrotonoyl-CoA + HCO3- = ADP + Orthophosphate +
3-Methylglutaconyl-CoA
SUBSTRATE ATP
3-Methylcrotonoyl-CoA
HCO3-
PRODUCT ADP
Orthophosphate
3-Methylglutaconyl-CoA
COFACTOR Biotin
COMMENT A biotinyl-protein.
PATHWAY PATH: MAP00280 Valine, leucine and isoleucine degradation
GENES HSA: MCCC1 MCCC2
DBLINKS University of Geneva ENZYME DATA BANK: 6.4.1.4
WIT (What Is There) Metabolic Reconstruction: 6.4.1.4
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