ENTRY       EC 6.3.4.9
NAME        Biotin--[methylmalonyl-CoA-carboxyltransferase] ligase
            Biotin-[methylmalonyl-CoA-carboxyltransferase] synthetase
CLASS       Ligases
            Forming carbon-nitrogen bonds
            Other carbon--nitrogen ligases
SYSNAME     Biotin:apo[methylmalonyl-CoA:pyruvate carboxyltransferase] ligase
            $ (AMP-forming)
REACTION    ATP + Biotin + Apo-[methylmalonyl-CoA:pyruvate
            $ carboxyltransferase] = AMP + Pyrophosphate + [Methylmalonyl-
            $CoA:pyruvate carboxyltransferase]
SUBSTRATE   ATP
            Biotin
            Apo-[methylmalonyl-CoA:pyruvate carboxyltransferase]
PRODUCT     AMP
            Pyrophosphate
            [Methylmalonyl-CoA:pyruvate carboxyltransferase]
DISEASE     MIM: 253270  Holocarbyoxylase synthetase; Multiple carboxylase
                         deficiency, biotin-responsive (3)
DBLINKS     University of Geneva ENZYME DATA BANK: 6.3.4.9
            WIT (What Is There) Metabolic Reconstruction: 6.3.4.9
///

DBGET integrated database retrieval system, GenomeNet