ENTRY EC 6.3.4.9
NAME Biotin--[methylmalonyl-CoA-carboxyltransferase] ligase
Biotin-[methylmalonyl-CoA-carboxyltransferase] synthetase
CLASS Ligases
Forming carbon-nitrogen bonds
Other carbon--nitrogen ligases
SYSNAME Biotin:apo[methylmalonyl-CoA:pyruvate carboxyltransferase] ligase
$ (AMP-forming)
REACTION ATP + Biotin + Apo-[methylmalonyl-CoA:pyruvate
$ carboxyltransferase] = AMP + Pyrophosphate + [Methylmalonyl-
$CoA:pyruvate carboxyltransferase]
SUBSTRATE ATP
Biotin
Apo-[methylmalonyl-CoA:pyruvate carboxyltransferase]
PRODUCT AMP
Pyrophosphate
[Methylmalonyl-CoA:pyruvate carboxyltransferase]
DISEASE MIM: 253270 Holocarbyoxylase synthetase; Multiple carboxylase
deficiency, biotin-responsive (3)
DBLINKS University of Geneva ENZYME DATA BANK: 6.3.4.9
WIT (What Is There) Metabolic Reconstruction: 6.3.4.9
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