ENTRY EC 4.3.1.3
NAME Histidine ammonia-lyase
Histidase
Histidinase
Histidine alpha-deaminase
CLASS Lyases
Carbon-nitrogen lyases
Ammonia-lyases
SYSNAME L-Histidine ammonia-lyase
REACTION L-Histidine = Urocanate + NH3
SUBSTRATE L-Histidine
PRODUCT Urocanate
NH3
PATHWAY PATH: MAP00340 Histidine metabolism
PATH: MAP00910 Nitrogen metabolism
DISEASE MIM: 235800 Histidine ammonia-lyase (histidase); [Histidinemia]
(1)
MOTIF PS: PS00488 G-[STG]-[LIVM]-[STG]-[AC]-S-G-[DH]-L-x-P-L-[SA]-x(2)-
[SA]
GENES BSU: hutH
HSA: HAL(HIS)
DBLINKS University of Geneva ENZYME DATA BANK: 4.3.1.3
WIT (What Is There) Metabolic Reconstruction: 4.3.1.3
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