ENTRY       EC 3.5.1.26
NAME        N4-(beta-N-Acetylglucosaminyl)-L-asparaginase
            Aspartylglucosylamine deaspartylase
            Aspartylglucosylaminase
CLASS       Hydrolases
            Acting on carbon-nitrogen bonds, other than peptide bonds
            In linear amides
SYSNAME     N4-(beta-N-Acetyl-D-glucosaminyl)-L-asparagine amidohydrolase
REACTION    N4-(beta-N-Acetyl-D-glucosaminyl)-L-asparagine + H2O =
            N-Acetyl-beta-D-glucosaminylamine + L-Aspartate
SUBSTRATE   N4-(beta-N-Acetyl-D-glucosaminyl)-L-asparagine
            H2O
PRODUCT     N-Acetyl-beta-D-glucosaminylamine
            L-Aspartate
COMMENT     Acts only on asparagine-oligosaccharides containing one amino
            acid, i.e. the asparagine has free alpha-amino and alpha-carboxyl
            groups. (cf. EC 3.5.1.52)
DISEASE     MIM: 208400  Aspartylglucosaminidase; Aspartylglucosaminuria (3)
GENES       HSA: AGA(Hs.21488)
STRUCTURES  PDB: 1APY  1APZ  
DBLINKS     University of Geneva ENZYME DATA BANK: 3.5.1.26
            WIT (What Is There) Metabolic Reconstruction: 3.5.1.26
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