ENTRY EC 3.5.1.12
NAME Biotinidase
CLASS Hydrolases
Acting on carbon-nitrogen bonds, other than peptide bonds
In linear amides
SYSNAME Biotin-amide amidohydrolase
REACTION Biotin amide + H2O = Biotin + NH3
SUBSTRATE Biotin amide
H2O
PRODUCT Biotin
NH3
COMMENT Also acts on biotin esters.
PATHWAY PATH: MAP00780 Biotin metabolism
DISEASE MIM: 253260 Biotinidase; Biotinidase deficiency (3)
GENES HSA: BTD(Hs.78885)
DBLINKS University of Geneva ENZYME DATA BANK: 3.5.1.12
WIT (What Is There) Metabolic Reconstruction: 3.5.1.12
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