ENTRY       EC 3.2.1.50
NAME        alpha-N-Acetylglucosaminidase
CLASS       Hydrolases
            Glycosidases
            Hydrolysing O-glycosyl compounds
SYSNAME     alpha-N-Acetyl-D-glucosaminide N-acetylglucosaminohydrolase
REACTION    Hydrolysis of terminal, non-reducing N-acetyl-D-glucosamine
            residues in N-acetyl-alpha-D-glucosaminides
SUBSTRATE   N-Acetyl-alpha-D-glucosaminide
            H2O
PRODUCT     N-Acetyl-D-glucosamine
COMMENT     HYdrolyses UDP-N-acetylglucosamine.
PATHWAY     PATH: MAP00530  Aminosugars metabolism
DISEASE     MIM: 252920  N-acetylglucosaminidase, alpha-; Sanfilippo syndrome,
                         type B (3)
GENES       HSA: NAGLU(NAG)
DBLINKS     University of Geneva ENZYME DATA BANK: 3.2.1.50
            WIT (What Is There) Metabolic Reconstruction: 3.2.1.50
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