ENTRY EC 3.2.1.50
NAME alpha-N-Acetylglucosaminidase
CLASS Hydrolases
Glycosidases
Hydrolysing O-glycosyl compounds
SYSNAME alpha-N-Acetyl-D-glucosaminide N-acetylglucosaminohydrolase
REACTION Hydrolysis of terminal, non-reducing N-acetyl-D-glucosamine
residues in N-acetyl-alpha-D-glucosaminides
SUBSTRATE N-Acetyl-alpha-D-glucosaminide
H2O
PRODUCT N-Acetyl-D-glucosamine
COMMENT HYdrolyses UDP-N-acetylglucosamine.
PATHWAY PATH: MAP00530 Aminosugars metabolism
DISEASE MIM: 252920 N-acetylglucosaminidase, alpha-; Sanfilippo syndrome,
type B (3)
GENES HSA: NAGLU(NAG)
DBLINKS University of Geneva ENZYME DATA BANK: 3.2.1.50
WIT (What Is There) Metabolic Reconstruction: 3.2.1.50
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