ENTRY EC 3.2.1.46
NAME Galactosylceramidase
CLASS Hydrolases
Glycosidases
Hydrolysing O-glycosyl compounds
SYSNAME D-Galactosyl-N-acylsphingosine galactohydrolase
REACTION D-Galactosyl-N-acylsphingosine + H2O = D-Galactose +
N-Acylsphingosine
SUBSTRATE D-Galactosyl-N-acylsphingosine
H2O
PRODUCT D-Galactose
N-Acylsphingosine
COMMENT cf. EC 3.2.1.62.
DISEASE MIM: 245200 Galactosylceraminidase; Krabbe disease (3)
GENES HSA: GALC(Hs.273)
DBLINKS University of Geneva ENZYME DATA BANK: 3.2.1.46
WIT (What Is There) Metabolic Reconstruction: 3.2.1.46
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