ENTRY       EC 3.2.1.46
NAME        Galactosylceramidase
CLASS       Hydrolases
            Glycosidases
            Hydrolysing O-glycosyl compounds
SYSNAME     D-Galactosyl-N-acylsphingosine galactohydrolase
REACTION    D-Galactosyl-N-acylsphingosine + H2O = D-Galactose +
            N-Acylsphingosine
SUBSTRATE   D-Galactosyl-N-acylsphingosine
            H2O
PRODUCT     D-Galactose
            N-Acylsphingosine
COMMENT     cf. EC 3.2.1.62.
DISEASE     MIM: 245200  Galactosylceraminidase; Krabbe disease (3)
GENES       HSA: GALC(Hs.273)
DBLINKS     University of Geneva ENZYME DATA BANK: 3.2.1.46
            WIT (What Is There) Metabolic Reconstruction: 3.2.1.46
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