ENTRY       EC 2.7.1.3
NAME        Ketohexokinase
CLASS       Transferases
            Transferring phosphorus-containing groups
            Phosphotransferases with an alcohol group as acceptor
SYSNAME     ATP:D-fructose 1-phosphotransferase
REACTION    ATP + D-Fructose = ADP + D-Fructose 1-phosphate
SUBSTRATE   ATP
            D-Fructose
            D-Sorbose
            D-Agatose
            5-Dehydro-D-fructose
PRODUCT     ADP
            D-Fructose 1-phosphate
COMMENT     D-Sorbose, D-agatose and 5-dehydro-D-fructose also act as
            acceptors
PATHWAY     PATH: MAP00051  Fructose and mannose metabolism
DISEASE     MIM: 229800  Ketohexokinase (fructokinase); [Fructosuria] (1)
GENES       HSA: KHK(Hs.81454)
DBLINKS     University of Geneva ENZYME DATA BANK: 2.7.1.3
            WIT (What Is There) Metabolic Reconstruction: 2.7.1.3
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