ENTRY EC 3.5.4.6
NAME AMP deaminase
Adenylic acid deaminase
AMP aminase
CLASS Hydrolases
Acting on carbon-nitrogen bonds, other than peptide bonds
In cyclic amidines
SYSNAME AMP aminohydrolase
REACTION AMP + H2O = IMP + NH3
SUBSTRATE AMP
H2O
PRODUCT IMP
NH3
COMMENT (cf. EC 3.5.4.17)
PATHWAY PATH: MAP00230 Purine metabolism
DISEASE MIM: 102770 Adenosine monophosphate deaminase-1 (muscle);
Myoadenylate deaminase deficiency (3)
MIM: 102771 Adenosine monophosphate deaminase-2 (isoform L)
MIM: 102772 Adenosine monophosphate deaminase 3 (isoform E); [AMP
deaminase deficiency, erythrocytic] (3)
MOTIF PS: PS00485 S-[LIVM]-[NS]-T-D-D-P
GENES SCE: YML035C(AMD1)
HSA: AMPD1 AMPD2 AMPD3(Hs.83918)
DBLINKS University of Geneva ENZYME DATA BANK: 3.5.4.6
WIT (What Is There) Metabolic Reconstruction: 3.5.4.6
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