ENTRY       EC 3.5.1.12
NAME        Biotinidase
CLASS       Hydrolases
            Acting on carbon-nitrogen bonds, other than peptide bonds
            In linear amides
SYSNAME     Biotin-amide amidohydrolase
REACTION    Biotin amide + H2O = Biotin + NH3
SUBSTRATE   Biotin amide
            H2O
PRODUCT     Biotin
            NH3
COMMENT     Also acts on biotin esters.
PATHWAY     PATH: MAP00780  Biotin metabolism
DISEASE     MIM: 253260  Biotinidase; Biotinidase deficiency (3)
GENES       HSA: BTD(Hs.78885)
DBLINKS     University of Geneva ENZYME DATA BANK: 3.5.1.12
            WIT (What Is There) Metabolic Reconstruction: 3.5.1.12
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