ENTRY EC 2.7.6.1
NAME Ribose-phosphate pyrophosphokinase
CLASS Transferases
Transferring phosphorus-containing groups
Diphosphotransferases
SYSNAME ATP:D-ribose-5-phosphate pyrophosphotransferase
REACTION ATP + D-Ribose 5-phosphate = AMP +
5-Phospho-alpha-D-ribose 1-diphosphate
SUBSTRATE ATP
dATP
D-Ribose 5-phosphate
PRODUCT AMP
dAMP
5-Phospho-alpha-D-ribose 1-diphosphate
COMMENT dATP can also act as donor
PATHWAY PATH: MAP00030 Pentose phosphate cycle
PATH: MAP00230 Purine metabolism
DISEASE MIM: 311850 Phosphoribosyl pyrophosphate synthetase-1;
Phosphoribosyl pyrophosphate synthetase-related gout
(3)
MIM: 311860 Phosphoribosyl pyrophosphate synthetase 2
MOTIF PS: PS00114 D-L-H-A-x-Q-[IM]-Q-G-F-F-x(2)-P-[LIVM]-D
GENES MJA: MJ1366
MTH: MTH784
ECO: b1207(prsA)
HIN: HI1609(prsA)
HPY: HP0742(prsA)
BSU: prs
MGE: MG058(prsA)
MPN: D09_orf388(prsA)
SYN: sll0469(prsA)
SCE: YBL068W(PRPS4) YER099C(PRPS2) YHL011C(PRPS3) YKL181W(PRPS1)
DBLINKS University of Geneva ENZYME DATA BANK: 2.7.6.1
WIT (What Is There) Metabolic Reconstruction: 2.7.6.1
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